Online 2016 ICD-10-CM · Tabular List · Alpha Index · ICD-9/ICD-10 conversion · ICD-10-PCS



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ICD-9 code:

2703

Disturbances of branched-chain amino-acid metabolism

ICD-10 codeDescriptionGEM flags set *
E71.0Maple-syrup-urine diseaseApproximate Flag
E71.120Methylmalonic acidemiaApproximate Flag
E71.19Other disorders of branched-chain amino-acid metabolismApproximate Flag
E71.2Disorder of branched-chain amino-acid metabolism, unspecifiedApproximate Flag

* See General Equivalence Mappings (GEMs) FAQ (pdf) for more information on GEM flag values.