Online 2016 ICD-10-CM · Tabular List · Alpha Index · ICD-9/ICD-10 conversion · ICD-10-PCS


 E75 - Disorders of sphingolipid metabolism and other lipid storage disorders

Excludes 1:
-mucolipidosis, types I-III E77.0-E77.1)
-Refsum's disease G60.1)


 E75.0 - GM2 gangliosidosis
 E75.00 - GM2 gangliosidosis, unspecified
 E75.01 - Sandhoff disease
 E75.02 - Tay-Sachs disease
 E75.09 - Other GM2 gangliosidosis
 E75.1 - Other and unspecified gangliosidosis
 E75.10 - Unspecified gangliosidosis
 E75.11 - Mucolipidosis IV
 E75.19 - Other gangliosidosis
 E75.2 - Other sphingolipidosis
 E75.21 - Fabry (-Anderson) disease
 E75.22 - Gaucher disease
 E75.23 - Krabbe disease
 E75.24 - Niemann-Pick disease
 E75.240 - Niemann-Pick disease type A
 E75.241 - Niemann-Pick disease type B
 E75.242 - Niemann-Pick disease type C
 E75.243 - Niemann-Pick disease type D
 E75.248 - Other Niemann-Pick disease
 E75.249 - Niemann-Pick disease, unspecified
 E75.25 - Metachromatic leukodystrophy
 E75.29 - Other sphingolipidosis
 E75.3 - Sphingolipidosis, unspecified
 E75.4 - Neuronal ceroid lipofuscinosis
 E75.5 - Other lipid storage disorders
 E75.6 - Lipid storage disorder, unspecified