E71 - Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
E71.3 - Disorders of fatty-acid metabolism
Excludes 1:
-peroxisomal disorders E71.5)
-Refsum's disease G60.1)
-Schilder's disease G37.0)
Excludes 2:
-carnitine deficiency due to inborn error of metabolism E71.42)
E71.30 - Disorder of fatty-acid metabolism, unspecified
E71.31 - Disorders of fatty-acid oxidation
E71.310 - Long chain/very long chain acyl CoA dehydrogenase deficiency
E71.311 - Medium chain acyl CoA dehydrogenase deficiency
E71.312 - Short chain acyl CoA dehydrogenase deficiency
E71.313 - Glutaric aciduria type II
E71.314 - Muscle carnitine palmitoyltransferase deficiency
E71.318 - Other disorders of fatty-acid oxidation
E71.32 - Disorders of ketone metabolism
E71.39 - Other disorders of fatty-acid metabolism