D56 - Thalassemia
D56.0 - Alpha thalassemia
InclusionTerm:
-Alpha thalassemia major
-Hemoglobin H Constant Spring
-Hemoglobin H disease
-Hydrops fetalis due to alpha thalassemia
-Severe alpha thalassemia
-Triple gene defect alpha thalassemia
Use Additional Code:
-code, if applicable, for hydrops fetalis due to alpha thalassemia P56.99)
Excludes 1:
-alpha thalassemia trait or minor D56.3)
-asymptomatic alpha thalassemia D56.3)
-hydrops fetalis due to isoimmunization P56.0)
-hydrops fetalis not due to immune hemolysis P83.2)