| M30 | Polyarteritis nodosa and related conditions |
| M30.0 | Polyarteritis nodosa |
| M30.1 | Polyarteritis with lung involvement [Churg-Strauss] |
| M30.2 | Juvenile polyarteritis |
| M30.3 | Mucocutaneous lymph node syndrome [Kawasaki] |
| M30.8 | Other conditions related to polyarteritis nodosa |
| M31 | Other necrotizing vasculopathies |
| M31.0 | Hypersensitivity angiitis |
| M31.1 | Thrombotic microangiopathy |
| M31.2 | Lethal midline granuloma |
| M31.3 | Wegener's granulomatosis |
| M31.30 | Wegener's granulomatosis without renal involvement |
| M31.31 | Wegener's granulomatosis with renal involvement |
| M31.4 | Aortic arch syndrome [Takayasu] |
| M31.5 | Giant cell arteritis with polymyalgia rheumatica |
| M31.6 | Other giant cell arteritis |
| M31.7 | Microscopic polyangiitis |
| M31.8 | Other specified necrotizing vasculopathies |
| M31.9 | Necrotizing vasculopathy, unspecified |
| M32 | Systemic lupus erythematosus (SLE) |
| M32.0 | Drug-induced systemic lupus erythematosus |
| M32.1 | Systemic lupus erythematosus with organ or system involvement |
| M32.10 | Systemic lupus erythematosus, organ or system involvement unspecified |
| M32.11 | Endocarditis in systemic lupus erythematosus |
| M32.12 | Pericarditis in systemic lupus erythematosus |
| M32.13 | Lung involvement in systemic lupus erythematosus |
| M32.14 | Glomerular disease in systemic lupus erythematosus |
| M32.15 | Tubulo-interstitial nephropathy in systemic lupus erythematosus |
| M32.19 | Other organ or system involvement in systemic lupus erythematosus |
| M32.8 | Other forms of systemic lupus erythematosus |
| M32.9 | Systemic lupus erythematosus, unspecified |
| M33 | Dermatopolymyositis |
| M33.0 | Juvenile dermatopolymyositis |
| M33.00 | Juvenile dermatopolymyositis, organ involvement unspecified |
| M33.01 | Juvenile dermatopolymyositis with respiratory involvement |
| M33.02 | Juvenile dermatopolymyositis with myopathy |
| M33.09 | Juvenile dermatopolymyositis with other organ involvement |
| M33.1 | Other dermatopolymyositis |
| M33.10 | Other dermatopolymyositis, organ involvement unspecified |
| M33.11 | Other dermatopolymyositis with respiratory involvement |
| M33.12 | Other dermatopolymyositis with myopathy |
| M33.19 | Other dermatopolymyositis with other organ involvement |
| M33.2 | Polymyositis |
| M33.20 | Polymyositis, organ involvement unspecified |
| M33.21 | Polymyositis with respiratory involvement |
| M33.22 | Polymyositis with myopathy |
| M33.29 | Polymyositis with other organ involvement |
| M33.9 | Dermatopolymyositis, unspecified |
| M33.90 | Dermatopolymyositis, unspecified, organ involvement unspecified |
| M33.91 | Dermatopolymyositis, unspecified with respiratory involvement |
| M33.92 | Dermatopolymyositis, unspecified with myopathy |
| M33.99 | Dermatopolymyositis, unspecified with other organ involvement |
| M34 | Systemic sclerosis [scleroderma] |
| M34.0 | Progressive systemic sclerosis |
| M34.1 | CR(E)ST syndrome |
| M34.2 | Systemic sclerosis induced by drug and chemical |
| M34.8 | Other forms of systemic sclerosis |
| M34.81 | Systemic sclerosis with lung involvement |
| M34.82 | Systemic sclerosis with myopathy |
| M34.83 | Systemic sclerosis with polyneuropathy |
| M34.89 | Other systemic sclerosis |
| M34.9 | Systemic sclerosis, unspecified |
| M35 | Other systemic involvement of connective tissue |
| M35.0 | Sicca syndrome [Sjögren] |
| M35.00 | Sicca syndrome, unspecified |
| M35.01 | Sicca syndrome with keratoconjunctivitis |
| M35.02 | Sicca syndrome with lung involvement |
| M35.03 | Sicca syndrome with myopathy |
| M35.04 | Sicca syndrome with tubulo-interstitial nephropathy |
| M35.09 | Sicca syndrome with other organ involvement |
| M35.1 | Other overlap syndromes |
| M35.2 | Behçet's disease |
| M35.3 | Polymyalgia rheumatica |
| M35.4 | Diffuse (eosinophilic) fasciitis |
| M35.5 | Multifocal fibrosclerosis |
| M35.6 | Relapsing panniculitis [Weber-Christian] |
| M35.7 | Hypermobility syndrome |
| M35.8 | Other specified systemic involvement of connective tissue |
| M35.9 | Systemic involvement of connective tissue, unspecified |
| M36 | Systemic disorders of connective tissue in diseases classified elsewhere |
| M36.0 | Dermato(poly)myositis in neoplastic disease |
| M36.1 | Arthropathy in neoplastic disease |
| M36.2 | Hemophilic arthropathy |
| M36.3 | Arthropathy in other blood disorders |
| M36.4 | Arthropathy in hypersensitivity reactions classified elsewhere |
| M36.8 | Systemic disorders of connective tissue in other diseases classified elsewhere |