| E73 | Lactose intolerance |
| E73.0 | Congenital lactase deficiency |
| E73.1 | Secondary lactase deficiency |
| E73.8 | Other lactose intolerance |
| E73.9 | Lactose intolerance, unspecified |
| E74 | Other disorders of carbohydrate metabolism |
| E74.0 | Glycogen storage disease |
| E74.00 | Glycogen storage disease, unspecified |
| E74.01 | von Gierke disease |
| E74.02 | Pompe disease |
| E74.03 | Cori disease |
| E74.04 | McArdle disease |
| E74.09 | Other glycogen storage disease |
| E74.1 | Disorders of fructose metabolism |
| E74.10 | Disorder of fructose metabolism, unspecified |
| E74.11 | Essential fructosuria |
| E74.12 | Hereditary fructose intolerance |
| E74.19 | Other disorders of fructose metabolism |
| E74.2 | Disorders of galactose metabolism |
| E74.20 | Disorders of galactose metabolism, unspecified |
| E74.21 | Galactosemia |
| E74.29 | Other disorders of galactose metabolism |
| E74.3 | Other disorders of intestinal carbohydrate absorption |
| E74.31 | Sucrase-isomaltase deficiency |
| E74.39 | Other disorders of intestinal carbohydrate absorption |
| E74.4 | Disorders of pyruvate metabolism and gluconeogenesis |
| E74.8 | Other specified disorders of carbohydrate metabolism |
| E74.9 | Disorder of carbohydrate metabolism, unspecified |